Evans Syndrome: A Rare Autoimmune Disorder
Symptoms and Causes of Evans Syndrome
Evans syndrome is a rare autoimmune disorder that occurs when the immune system mistakenly attacks one's own blood cells, specifically red blood cells (RBCs), platelets, and less commonly, white blood cells (WBCs).
Symptoms of Evans syndrome can vary depending on which blood cells are affected and can include:
- Purpura (purple-colored spots on the skin due to bleeding)
- Paleness (due to anemia)
- Fatigue (due to low RBC count and anemia)
- Light-headedness (due to low blood pressure)
- Fever (due to the immune response)
- Malaise (general feeling of poor health)
- Sores or ulcers on the mucous membranes of the mouth
The exact cause of Evans syndrome is unknown, but it is believed to be triggered by an immune system malfunction.
Treatment and Outlook
Treatment for Evans syndrome typically involves suppressing the immune system and preventing further destruction of blood cells. This may include:
- Immunosuppressive drugs
- Intravenous immunoglobulin (IVIG)
- Plasmapheresis
- Blood transfusions
The outlook for people with Evans syndrome varies depending on the severity of their condition and how well they respond to treatment. With proper management, many people with Evans syndrome can live full and active lives.
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